Nice Article - Bicuspid Aortic Valve Repair: Bryan’s Story

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[h=1]Bicuspid Aortic Valve Repair: Bryan’s Story[/h] http://www.dailylocal.com/article/DL/20180205/NEWS/180209896

By Barbara Curtis

A collegiate athlete turned physical education teacher, Bryan Tingle has been physically active his entire life. He was an accomplished lacrosse player and even tried out for professional leagues, like the New York Titans. At 34-years-old, he continued his fit lifestyle, completing triathlons while keeping up with three young children at home – until one day he experienced an uncomfortable sensation.

“I was running over the summer and could feel my heart beating differently. It was a strange feeling – it didn’t hurt but I knew something wasn’t right,” said Tingle.

He was a young, healthy guy with no known medical issues, other than a heart murmur he was diagnosed with at the age of 11. “The murmur never had an impact on my life, so I figured the palpitation was from everyday stress,” added Tingle.

Five days later, he continued to feel palpitations along with chest pressure. His wife insisted he go to an urgent care facility for peace of mind. The clinicians detected unusually high blood pressure and his electrocardiogram (EKG) was abnormal – they immediately called an ambulance in fear he was having a heart attack.


Tingle was rushed to Chester County Hospital’s Emergency Department, where a team of doctors and nurse practitioners evaluated his condition. Multiple tests were performed and Tingle was relieved to learn he had not experienced a heart attack. His lab work was good, a second EKG was normal, and the test results determined he had not suffered any damage to his heart. He was released and told to schedule an appointment with a cardiologist.

With this good news, he went on a family vacation to the Outer Banks, North Carolina with his three children and wife, who was expecting their fourth child. But once he was there, he began feeling chest pain and immediately went to the local emergency room. Their diagnosis – a panic attack.

Having two emergency room visits within weeks of each other was concerning for Tingle, especially with a fourth baby on the way. As soon as he returned home, he made an appointment with his cardiologist, Dr. Mian Jan at West Chester Cardiology. Dr. Jan ordered a Transesophageal Echocardiogram (TEE).

A TEE is a special type of echocardiogram that produces detailed images of the heart’s structure by using a thin tube that goes down the esophagus. Since the esophagus is close to the upper chambers of the heart, physicians have a clearer, more detailed view of these chambers than from a traditional echocardiogram.

The results confirmed Tingle was not experiencing symptoms of a panic attack, but in fact, had a congenital heart condition (from birth). Tingle had a bicuspid aortic valve, meaning his aortic valve only had two leaflets instead of three and was leaking severely.

A healthy aortic valve has three cusps or leaflets – known as a tricuspid valve – which open and close to regulate blood flow. Oftentimes a bicuspid valve will work well for many years, only beginning to show symptoms later in adulthood.

In Tingle’s case, the TEE showed that the symptoms he was experiencing were a result of the leaky aortic valve, which caused blood to flow back into the heart instead of flowing forward. When this occurs, the heart muscle weakens since it must work harder to pump blood throughout the body. If left untreated, it can lead to dilation of the aortic valve and left ventricle causing irreversible damage and heart failure.

Dr. Jan referred him to the Heart Valve Center at Chester County Hospital. For Tingle’s consultation, Steven Weiss, MD, chief of Cardiac Surgery, invited Nimesh Desai, MD, PhD, director of the Thoracic Aortic Surgery Research Program at the Hospital of the University of Pennsylvania (HUP), to join him in evaluating this complex case.

“It was a scary experience knowing I had a heart condition that was causing my symptoms. But when I met with Dr. Weiss and Dr. Desai, I knew I was in good hands. They were very reassuring and made me comfortable,” says Tingle.

Depending on each patient’s unique situation, there are a few surgical procedures available to correct a valve condition. The first is a mechanical aortic valve replacement, which provides a durable, long-lasting solution but requires patients to take Coumadin, a blood thinner, for the remainder of their life. The second option is a tissue aortic valve replacement, which does not require long-term use of medication but at Tingle’s age could only be expected to last between 10 and 15 years.

The third and best option is an aortic valve repair. Patients who have a valve repair do not require lifelong medication or future surgeries. Fortunately for Tingle, his surgeons were confident they could successfully repair his aortic valve.

“We performed an advanced repair that only a few places in the country are doing. It’s called a bicuspid aortic valve repair with Lansac ring. The ring sits outside of the aorta, underneath the coronary arteries, and prevents the repaired aortic valve from ever dilating. It’s a new refinement of the leaflet repair procedure intended to provide lifetime durability, which was a perfect fit for a young individual like Mr. Tingle,” said Dr. Weiss.

As the surgery was being finished, Tingle was taken off of the heart and lung machine, often called “the pump,” and was in excellent condition. But shortly after, his aorta developed a tear resulting in blood loss.

The issue was detected immediately and his care team worked together to cool his body, get him back on the pump and fix the tear. After living with a heart condition for over thirty years, his aorta had become very thin and prone to a complication.

“What makes a program great is not the absence of complication, but eliminating failure to rescue. Detecting and correcting a problem early, so that no harm occurs to the patient, is what makes a hospital have great outcomes,” added Dr. Weiss.

Typically only available at HUP, along with a few other facilities in the U.S., the procedure was successfully performed by Dr. Weiss and Dr. Desai at Chester County Hospital.

Today, Tingle is in better physical condition than ever before and is able to live a life without restrictions just 12 weeks after his surgery.

“I can’t say enough positive things about my experience. The surgeons, nurses and the team at cardiac rehabilitation all took great care of me. My priorities have changed since the surgery because I’ve been given another chance to live without fear of my heart condition. I’m looking forward to spending more time with my family, my students… and living an active life with them again. God has a lot in store for me,” added Tingle.

Mian Jan, MD, FACC is also chairman of Chester County Hospital’s department of medicine.
 
Wow!! As a young person with BAV this is extremely encouraging!! Can anyone inform me further or point me in the direction of info detailing patients who are good candidates for this surgery or repairs as apposed to replacements? They’ve always made it seem like replacement was the only option and I figured that was true since most high profile, wealthy ppl with BAV still get OHS to replace. Thanks for sharing .
 
Repair vs. replace is really something only you, your cardiologist, and most of all your surgeon can determine. You can always ask your care team. It's very much a case by case basis and I wouldn't expect you could point to any one individual and say, "They did it, why can't I?". It really depends on your own presentation.

When I was a kid, they talked about doing a balloon angioplasty. They would place a balloon in the valve via catheter, then inflate to open the valve more and alleviate the severe stenosis I had. Ultimately this was not done. I don't know exactly why. Possibly due to the leaking I already had as well, which didn't make me a good candidate.

Do your research now. Look up medical reviews. Try to find a cardiologist that specializes in adults with congenital heart defects. They will understand your condition better than a cardiologist who deals primarily with congestive heart failure, blocked arteries, or other common aging ailments.
 
Superman;n881563 said:
Repair vs. replace is really something only you, your cardiologist, and most of all your surgeon can determine. You can always ask your care team. It's very much a case by case basis and I wouldn't expect you could point to any one individual and say, "They did it, why can't I?". It really depends on your own presentation.

When I was a kid, they talked about doing a balloon angioplasty. They would place a balloon in the valve via catheter, then inflate to open the valve more and alleviate the severe stenosis I had. Ultimately this was not done. I don't know exactly why. Possibly due to the leaking I already had as well, which didn't make me a good candidate.

Do your research now. Look up medical reviews. Try to find a cardiologist that specializes in adults with congenital heart defects. They will understand your condition better than a cardiologist who deals primarily with congestive heart failure, blocked arteries, or other common aging ailments.

Agree 100% . The ability to repair the valve and the longevity of the repair is very dependant on the valve condition and the surgeon.
 
Jmprosser.lab it is difficult question to answer as this procedure is evolving as they gain more and more experience. And it will never be clear until you are closer to surgery and until they actually see your valve during the procedure. Svensson at Cleveland tends to say about 70% of patients that they feel could be candidates for a repair actually get a repair. While there are many variables which your surgeons will carefully evaluate the one that is a non starter is stenosis, if the valve is calcified then a repair is today not feasible.

What you need to keep in mind is that this field is maturing rapidly and the results (already very good in high volume centers) are getting better and better as they gain more experience. But at the end of the day a repair only makes sense if they feel confident that there is a good chance it will last more than 15 years. This is because the alternative is so good and a such the hurdle is quite high.

And you should take comfort in this as the alternative, if they cannot repair, is excellent. I recently posted the results from Yale over more than 20 years which shows that life expectancy after valve replacement is comparable to the age matched general population. And this covers the entire patient population, whereas BAV patients tend to have better results than they are generally younger/healthier than the average valve replacement candidate.

Hopefully you are many years away from some form of intervention, if it comes to that. But know that TODAY you have excellent options that will allow you to live a very long and healthy life.
 
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